therapeuticЮжно-Российский журнал терапевтической практикиSouth Russian Journal of Therapeutic Practice2712-81563033-8344РостГМУ10.21886/2712-8156-2026-7-2-69-75therapeutic-700Research ArticleКЛИНИЧЕСКИЕ СЛУЧАИCLINICAL CASESПациент с неоперированным единственным левым желудочком: клинический разборPatient with an unoperated single left ventricle: a clinical case reviewhttps://orcid.org/0000-0001-9290-5330ШеметоваГ. Н.ShemetovaG. N.

Шеметова Галина Николаевна, д. м. н., профессор, заведующий кафедрой поликлинической терапии, общей врачебной практики и профилактической медицины

Саратов

Galina N. Shemetova, Dr. Sci. (Med.), Professor, Professor Head of Outpatient Therapy, General Practice and Preventive Medicine

Saratov

Nenadyk@yandex.ruhttps://orcid.org/0009-0002-7744-4155СураеваВ. А.SuraevaV. A.

Сураева Валентина Алексеевна, ассистент кафедры поликлинической терапии, общей врачебной практики и профилактической медицины

Саратов

Valentina A. Suraeva, assistant Professor of Outpatient Therapy, General Practice and Preventive Medicine

Saratov

for.students.polik@mail.ruhttps://orcid.org/0009-0008-7181-2459МолодцовР. Н.MolodtsovR. N.

Молодцов Роман Николаевич, к. м. н., доцент кафедры поликлинической терапии, общей врачебной практики и профилактической медицины 

Саратов

Roman N. Molodtsov, Cand. Sci. (Med.), Associate Professor of Outpatient Therapy, General Practice and Preventive Medicine

Saratov

rdmo-molodcovrn@yandex.ruhttps://orcid.org/0009-0000-2005-1655НемцеваЛ. А.NemtsevaL. A.

Немцева Лада Андреевна, студентка 6-го курса Института клинической медицины по специальности «Лечебное дело»

Саратов

Lada A. Nemtseva, a 6th-year student at the Institute of Clinical Medicine, specializing in General Medicine

Saratov

soul339@mail.ruhttps://orcid.org/0009-0008-6093-9809СамсоновИ. Ю.SamsonovI. Yu.

Самсонов Игорь Юрьевич, студент 6-го курса Института клинической медицины по специальности «Лечебное дело» 

Саратов

Igor Y. Samsonov, 6th year student of the Institute of Clinical Medicine, specialty “Medical Science”

Saratov

seeyousgmu@mail.ruФГБОУ ВО «Саратовский государственный медицинский университет им. В.И. Разумовского» Минздрава РоссииРоссияSaratov State Medical University n. a. V.I. RazumovskyRussian Federation202625062026726975Copyright © Шеметова Г.Н., Сураева В.А., Молодцов Р.Н., Немцева Л.А., Самсонов И.Ю., 20262026Шеметова Г.Н., Сураева В.А., Молодцов Р.Н., Немцева Л.А., Самсонов И.Ю.Shemetova G.N., Suraeva V.A., Molodtsov R.N., Nemtseva L.A., Samsonov I.Y.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://www.therapeutic-j.ru/jour/article/view/700

Врождённый порок сердца в виде единственного левого желудочка — редкая врождённая патология, клинический прогноз которой напрямую зависит от своевременного хирургического вмешательства. У некоторых пациентов анатомические особенности порока уравновешивают лёгочный и системный кровотоки что позволяет им доживать до зрелого возраста без оперативного лечения. Разбор данного клинического случая направлен на демонстрацию такого пациента, дожившего до возраста 29 лет, но с неблагоприятным исходом из-за дополнительных отягчающих факторов.

Congenital heart disease in the form of a single left ventricle is a rare congenital pathology, the clinical prognosis of which directly depends on timely surgical intervention. In some patients, the anatomical features of the defect balance pulmonary and systemic blood flow, allowing them to survive into adulthood without surgery. This clinical case report aims to present such a patient, who survived to the age of 29, but with an unfavorable outcome due to additional complicating factors.

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The authors declare that there are no conflicts of interest present.