Primary exudative enteropathy: a clinical case
https://doi.org/10.21886/2712-8156-2021-2-2-88-93
Abstract
Primary exudative enteropathy is a rare disease caused by the formation of lymphatic vessel abnormalities in the intestinal wall, the development of pathological lymph flow into the intestinal lumen, and increased loss of plasma proteins in the feces. The leading clinical syndrome of the disease is edema with the development of hypoalbuminemia and dysproteinemia. To establish the diagnosis, it took numerous studies with the exception of the patient’s pathology of the kidneys, liver, and inflammatory bowel diseases. The course of the disease was characterized by significant resistance to therapy.
About the Authors
I. Yu. StatsenkoStatsenko Igor Yurievich, Cand. Sci. (Med.), Associate Professor of the Department of Internal Medicine
Volgograd
O. Yu. Sviridenko
Sviridenko Oleg Yurievich, Cand. Sci. (Med.), Associate Professor of the Department of Internal Diseases
Volgograd
R. G. Myazin
Russian Federation
Myazin Roman Gennadievich, Cand. Sci. (Med.), Associate Professor of the Department of Internal Medicine
Volgograd
D. N. Emelyanov
Emelyanov Dmitry Nikolaevich, Cand. Sci. (Med.), Associate Professor of the Department of Internal Medicine
Volgograd
A. O. Sviridenko
Sviridenko Anton Olegovich, Assistant, Department of Internal Medicine
Volgograd
References
1. Freeman HJ, Nimmo M. Intestinal lymphangiectasia in adults. World J Gastrointest Oncol. 2011;3(2):19-23. DOI: 10.4251/wjgo.v3.i2.19
2. Парфенов А.И., Крумс Л.М. Энтеропатия с потерей белка. Терапевтический архив. 2017;89(2):4-9. DOI: 10.17116/terarkh20178924-9
3. Полякова С.И., Потапов А.С., Щербаков П.Л., Лохматов М.М., Рославцева Е.А. Первичная лимфангиэктазия тонкой кишки. Клин. мед. 2005;83(9):62-65. eLIBRARY ID: 9140697
4. Alshikho MJ, Talas JM, Noureldine SI, Zazou S, Addas A, Kurabi H, e al. Intestinal Lymphangiectasia: Insights on Management and Literature Review. Am J Case Rep. 2016;17:512-22. DOI: 10.12659/ajcr.899636
5. Vignes S., Bellanger J. Primary intestinal lymphangiectasia (Waldmann’s disease). Orphanet J. Rare Dis. 2008;3:5. DOI: 10.1186/1750-1172-3-5
6. Wen J, Tang Q, Wu J, Wang Y, Cai W. Primary intestinal lymphangiectasia: four case reports and a review of the literature. Dig Dis Sci. 2010;55(12):3466-72. DOI: 10.1007/s10620-010-1161-1
7. Смирнов А.В., Виноградова Т.В., Воронкова Е.В., Каюков И.Г., Нутфуллина Г.М., Трофименко И.И., и др. Первичная интестинальная лимфангиоэктазия (болезнь Вальдманна). Нефрология. 2010;14(2):78-84. eLIBRARY ID: 15164363
8. Surampalli V, Ramaswamy S, Surendran D, Bammigatti C, Swaminathan RP. Primary Intestinal Lymphangiectasia (Waldmann’s Disease) Presenting with Chylous Effusions in a 15-Year-Old. J Clin Diagn Res. 2017;11(8):OD17-OD18. DOI: 10.7860/JCDR/2017/29055.10522
9. Levitt DG, Levitt MD. Protein losing enteropathy: comprehensive review of the mechanistic association with clinical and subclinical disease states. Clin Exp Gastroenterol. 2017;10:147-168. DOI: 10.2147/CEG.S136803
10. Chen CP, Chao Y, Li CP, Lo WC, Wu CW, Tsay SH, et al. Surgical resection of duodenal lymphangiectasia: a case report. World J Gastroenterol. 2003;9(12):2880-2. DOI: 10.3748/wjg.v9.i12.2880
Review
For citations:
Statsenko I.Yu., Sviridenko O.Yu., Myazin R.G., Emelyanov D.N., Sviridenko A.O. Primary exudative enteropathy: a clinical case. South Russian Journal of Therapeutic Practice. 2021;2(2):88-93. (In Russ.) https://doi.org/10.21886/2712-8156-2021-2-2-88-93