Difficult case of right ventricular pathology diagnostics. Double-chamber right ventricle
https://doi.org/10.21886/2712-8156-2025-6-2-72-79
Abstract
Right ventricular pathology diagnostics often causes difficulties. The article presents a clinical case of difficulty in verifying a two-chamber right ventricle. A patient with a history of resection of aortic coarctation but uncorrected ventricular septal defect eventually developed high-velocity flows in the right ventricle cavity, diagnosed by transthoracic echocardiography, which were regarded as manifestations of intraventricular obstruction in hypertrophic cardiomyopathy of the right ventricle. During additional examination, discrepancies arose in establishing the final diagnosis. Differential diagnosis was made between hypertrophic cardiomyopathy of the right ventricle, non-compact cardiomyopathy of the right ventricle and a two-chamber right ventricle.
About the Authors
S. R. GutovaRussian Federation
Saida R. Gutova, Cand. Sci. (Med.), Department of Faculty Therapy
Maykop
V. V. Skibitsky
Russian Federation
Vitaly V. Skibitskiy, Dr. Sci. (Med.), Professor, the Head of the Department of Hospital Therapy
Krasnodar
A. V. Fendrikova
Russian Federation
Alexandra V. Fendrikova, Cand. Sci. (Med.), assistant professor, Department of Hospital Therapy
Krasnodar
References
1. Goor D.A., Lillehei C.W. Congenital malformations of the heart: embryology, anatomy, and operative considerations. 1st ed. New York: Grune and Stratton; 1975. ISBN: 10.0808908103
2. McAlpine WA. Heart and coronary arteries: an anatomical atlas for clinical diagnosis, radiological investigation, and surgical treatment. Berlin: Springer-Verlag; 1974. https://doi.org/10.1007/978-3-642-65983-6
3. Lorenz CH, Walker ES, Morgan VL, Klein SS, Graham TP Jr. Normal human right and left ventricular mass, systolic function, and gender differences by cine magnetic resonance imaging. J Cardiovasc Magn Reson. 1999;1(1):7-21. https://doi.org/10.3109/10976649909080829
4. Lang RM, Badano LP, Mor-Avi V, Afilalo J, Armstrong A, Ernande L, et al. Recommendations for cardiac chamber quantification by echocardiography in adults: an update from the American Society of Echocardiography and the European Association of Cardiovascular Imaging. J Am Soc Echocardiogr. 2015;28(1):1-39.e14. https://doi.org/10.1016/j.echo.2014.10.003
5. Gabrusenko S.A., Gudkova A.Ya., Koziolova N.A., Alexandrova S.A., Berseneva M.I., Gordeev M.L., et al. 2020 Clinical practice guidelines for Hypertrophic cardiomyopathy. Russian Journal of Cardiology. 2021;26(5):4541. (In Russ.) https://doi.org/10.15829/1560-4071-2021-4541
6. Oleynikov V.E., Donetskaya N.A., Vdovkin A.V., Babina A.V., Avdeeva I.V. Non-compact right ventricular myocardium – diagnostic and clinical features: A review. Terapevticheskii arkhiv. 2022;94(4):558-564. (In Russ.) https://doi.org/10.26442/00403660.2022.04.201482
7. Loukas M, Housman B, Blaak C, Kralovic S, Tubbs RS, Anderson RH. Double-chambered right ventricle: a review. Cardiovasc Pathol. 2013;22(6):417-423. https://doi.org/10.1016/j.carpath.2013.03.004
8. Hoffman P, Wójcik AW, Rózański J, Siudalska H, Jakubowska E, Włodarska EK, et al. The role of echocardiography in diagnosing double chambered right ventricle in adults. Heart. 2004;90(7):789-793. https://doi.org/10.1136/hrt.2003.017137
9. Stout KK, Daniels CJ, Aboulhosn JA, Bozkurt B, Broberg CS, Colman JM, et al. 2018 AHA/ACC Guideline for the Management of Adults With Congenital Heart Disease: A Report of the American College of Cardiology/American Heart Association Task Force on Clinical Practice Guidelines. J Am Coll Cardiol. 2019;73(12):e81-e192. Erratum in: J Am Coll Cardiol. 2019;73(18):2361-2362. https://doi.org/10.1016/j.jacc.2018.08.1029
10. Galderisi M, Cosyns B, Edvardsen T, Cardim N, Delgado V, Di Salvo G, et al. Standardization of adult transthoracic echocardiography reporting in agreement with recent chamber quantification, diastolic function, and heart valve disease recommendations: an expert consensus document of the European Association of Cardiovascular Imaging. Eur Heart J Cardiovasc Imaging. 2017;18(12):1301-1310. https://doi.org/10.1093/ehjci/jex244
Supplementary files
Review
For citations:
Gutova S.R., Skibitsky V.V., Fendrikova A.V. Difficult case of right ventricular pathology diagnostics. Double-chamber right ventricle. South Russian Journal of Therapeutic Practice. 2025;6(2):72-79. (In Russ.) https://doi.org/10.21886/2712-8156-2025-6-2-72-79