From infectious disease specialist to rheumatologist — difficulties in diagnosing autoinflammatory diseases using adult-onset Still’s disease an example
https://doi.org/10.21886/2712-8156-2025-6-3-96-102
Abstract
The article discusses the signs and diagnostic algorithm of autoinflammatory diseases, principles of therapy. Clinical manifestations and complications of adult-onset Still’s disease are discussed. The most serious complication of this pathology is macrophage activation syndrome. The data of the European clinical guidelines on the principles of treatment of adult-onset Still’s disease and drugs recommended for administration to patients with macrophage activation syndrome are presented. A clinical case of diagnosis of adult-onset Still’s disease in a 36-year-old woman is presented.
Keywords
Supporting agencies: The study had no sponsorship support
About the Authors
Z. D. Mikhailova
Municipal Clinical Hospital No. 38
Russian Federation
Russian Federation
Zinaida D. Mikhailova, Dr. Sci. (Med.), Assoc. Prof., Consulting Physician
Nizhny Novgorod
D. A. Bobrov
Municipal Clinical Hospital No. 38
Russian Federation
Russian Federation
Denis A. Bobrov, Physician
Nizhny Novgorod
D. V. Pivovarov
Municipal Clinical Hospital No. 38
Russian Federation
Russian Federation
Dmitry V. Pivovarov, Cand.Sci. (Med.), Physician
Nizhny Novgorod
J. V. Omarova
Municipal Clinical Hospital No. 38
Russian Federation
Russian Federation
Yulia V. Omarova, Cand. Sci. (Med.), Physician
Nizhny Novgorod
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Review
For citations:
Mikhailova Z.D., Bobrov D.A., Pivovarov D.V., Omarova J.V. From infectious disease specialist to rheumatologist — difficulties in diagnosing autoinflammatory diseases using adult-onset Still’s disease an example. South Russian Journal of Therapeutic Practice. 2025;6(3):96-102. (In Russ.) https://doi.org/10.21886/2712-8156-2025-6-3-96-102
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