Hirschsprung’s disease: current state of the problem, clinical observation
https://doi.org/10.21886/2712-8156-2025-6-2-101-105
Abstract
Hirschsprung's disease (HD) (congenital agangliosis of the colon) was isolated into an independent nosological unit in 1886 by the Copenhagen pediatrician Hirschsprung. This disease is diagnosed in children and adults. To date, the etiology and mechanisms of HD disease development have been revealed, effective methods of diagnosis, surgical treatment and conservative management of patients have been developed. Treatment can significantly improve the prognosis and quality of life of patients. The clinical observation of a patient with HD who underwent surgical treatment 16 years after the disease was detected is presented.
About the Authors
A. T. Marinchuk
Rostov State Medical University
Russian Federation
Russian Federation
Alexander T. Marinchuk, Cand. Sci. (Med.), Associate Professor of the Department of Internal Diseases No. 1
Rostov-on-Don
E. S. Pak
Rostov State Medical University; Rostov Regional Clinical Hospital
Russian Federation
Russian Federation
Ekaterina S. Pak, Cand. Sci. (Med.), Assistant of the Department of Reconstructive, Cardiovascular, Thoracic, Maxillofacial Surgery and Organ Transplantation; Head of the Gastroenterology Department, of the Regional Center of Surgery and Donor Coordination
Rostov-on-Don
T. M. Petrova
Rostov Regional Clinical Hospital
Russian Federation
Russian Federation
Tatyana M. Petrova, gastroenterologist of the Gastroenterology Department, of the Regional Center of Surgery and Donor Coordination
Rostov-on-Don
A. S. Kharkov
Rostov State Medical University
Russian Federation
Russian Federation
Alexander S. Kharkov, Cand. Sci. (Med.), Associate Professor of the Department of Internal Diseases No. 1
Rostov-on-Don
O. V. Bukhtin
Rostov Regional Clinical Hospital
Russian Federation
Russian Federation
Oleg V. Bukhtin, Therapist of the Gastroenterological Department of the Center for Surgery and Donation Coordination (regional)
Rostov-on-Don
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Supplementary files
Review
For citations:
Marinchuk A.T., Pak E.S., Petrova T.M., Kharkov A.S., Bukhtin O.V. Hirschsprung’s disease: current state of the problem, clinical observation. South Russian Journal of Therapeutic Practice. 2025;6(2):101-105. (In Russ.) https://doi.org/10.21886/2712-8156-2025-6-2-101-105
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